Natural History of Melorheostosis

Melorheostosis is a rare connective tissue disorder characterized by a sclerosing bone dysplasia. This disease affects one side of the body and is rarely bilateral. The disease is discovered upon episodes of pain, stiffness, joint contractures and sometimes deformities that occurs with time. In addition, rare signs such as edema, hyperpigmented skin patches, vascular tumors, and malformations have been reported. The picture of the disease in terms of locations, occurrence of pain and associated bone fragility is unknown.

Objective

The aim of the study is to provide a comprehensive picture of the clinical signs to help establish guidelines and assess the impact of pain.

For publications from this and other study groups, see our publication page.

Members of this Study Group

Name Expertise / Role Country
PI*: Martine Cohen-Solal rheumatologist, co-chair ECTS RBDAG France
Corinna Grasemann endocrinologist Germany
Gavin Clunie rheumatologist United Kingdom
Luca Sangiorgi endocrinologist, ERN BOND coordinator Italy
Mariya Cherenko endocrinologist, EuRREB data manager the Netherlands
Natasha Appelman-Dijkstra internist-endocrinologist, EuRREB coordinator the Netherlands
Thomas Funck-Brentano rheumatologist France
Willem Lems rheumatologist, ECTS board member the Netherlands

 

For more information regarding the study or if you are interested to contribute to this study, please contact registries@lumc.nl.

 

*The Principal Investigator (PI) is the lead applicant responsible for submitting the data request and initiating the study.